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Case Reports
. 2023 Feb 22:44:102.
doi: 10.11604/pamj.2023.44.102.37239. eCollection 2023.

[A rare case of botryoid sarcoma of the uterine cervix: case report]

[Article in French]
Mohamed Moukhlissi  1 , Soumya Samba  1 , Younesse Najioui  2 , Amal Bennani  2 , Soufiane Berhili  1 , Loubna Mezouar  1
Affiliations
Case Reports

[A rare case of botryoid sarcoma of the uterine cervix: case report]

[Article in French]
Mohamed Moukhlissi et al. Pan Afr Med J. .

Abstract
in English, French

Botryoid sarcoma is a subtype of rhabdomyosarcoma affecting soft tissues and exceptionally the cervix. We here report the case of an 18-year-old female patient presenting to the emergency department with a feeling of pelvic heaviness, metrorrhagia and urinary retention. Gynecological examination showed budding mass of the uterine cervix. The biopsy showed botryoid sarcoma. Radiological evaluation revealed heterodense cervico-isthmic corporeal mass measuring 97 / 87 mm, without adenopathies or effusions or tumors at other sites. Treatment involved neoadjuvant chemotherapy with vincristine - adriamycin and cyclophosphamide (V-A-C), followed by surgery (total hysterectomy without adnexal preservation). After a follow-up of 3 years, the patient is still in clinical and radiological remission.

Le sarcome botryoïde est une variante de rhabdomyosarcome qui touche les tissus mous dont la localisation au niveau du col utérin reste exceptionnelle, nous rapportons l´observation d´une patiente âgée de 18 ans qui consulte aux urgences pour une pesanteur pelvienne avec des métrorragies et une rétention urinaire. L´examen gynécologique a révélé une masse bourgeonnante du col utérin dont la biopsie a montré une localisation cervicale d´un sarcome botryoïde, le bilan radiologique a montré une masse corporéo-isthmique hétérodense de 97/87 mm, sans adénopathies ni épanchements ni localisations tumorales à distance. La prise en charge a consisté à une chimiothérapie néoadjuvante à base de vincristine - Adriamycine et cyclophosphamide (V-A-C), puis une chirurgie (hystérectomie totale sans conservation annexielle). Après un suivi de 3 ans, la patiente est toujours en rémission clinique et radiologique.

Keywords: Rhabdomyosarcoma; botryoid; case report; uterine cervix.

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Conflict of interest statement

Les auteurs ne déclarent aucun conflit d´intérêts.

Figures

Figure 1
Figure 1
coupe de TDM abdomino-pelvienne montrant une masse corporéo-isthmique hétérodense de 97 / 87 mm, sans adénopathies ni épanchements
Figure 2
Figure 2
un aspect histologique d´un rhabdomyosarcome (RMS) de type embryonnaire
See this image and copyright information in PMC

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