Desmoid Tumor of the Posterior Neck: A Case Report

Abstract

Desmoid tumors are rare. They account for roughly 0.03% of all neoplasms and less than 3% of all soft tissue tumors. They are locally aggressive tumors with no known metastatic potential or dedifferentiation. A 29-year-old woman with no family history of neoplasms presented with a mass in the cervical region and moderate pain that had developed a year before. The patient underwent marginal resection of the bilateral posterior and lateral compartments of the neck. The histopathological report confirmed the diagnosis of desmoid tumor with nuclear positivity for beta-catenin. The patient received radiotherapy but did not show a favorable response; she has stable disease and takes colchicine at one-year follow-up.

Keywords: Aggressive fibromatosis; Desmoid tumor; Head and neck; Treatment.

Fig. 1

A Preoperative clinical aspect shows a large mass in the posterior region of the neck. B CAT scan reveals posterior muscle involvement. C and D Intraoperative images of exposed lesion and bilateral tumor resection

Fig. 2

A CT scan shows complete resection on the right side, partial response and stable disease on the left side B Clinical response to multidisciplinary treatment

Fig. 3

Photo Micrograph of lesion with the nuclear mark of beta-catenin (40 ×)