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Case Reports
. 2023 May 1:15:101855.
doi: 10.1016/j.jaccas.2023.101855. eCollection 2023 Jun 7.

A Phenomenal Binomaly: 2 Rare Diseases Presenting With Electrical Storm

Alvan Buckley  1 , Muhammad Ajlan  1 , Jay Maxwell  2 , Omid Salehian  1
Affiliations
Case Reports

A Phenomenal Binomaly: 2 Rare Diseases Presenting With Electrical Storm

Alvan Buckley et al. JACC Case Rep. .

Abstract

A previously well 34-year-old man presents with electrical storm after performing headstands. A step-by-step review of clinical information and case development is presented with discussion. Ultimately, 2 rare diagnoses are discovered and their potential contribution to a cascade of complications resulting in ventricular arrhythmia are discussed. (Level of Difficulty: Intermediate.).

Keywords: congenital heart disease; pheochromocytoma; ventricular tachycardia.

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Conflict of interest statement

The authors have reported that they have no relationships relevant to the contents of this paper to disclose.

Figures

None
Graphical abstract
Figure 1
Figure 1
Electrocardiogram Demonstrating Diffuse Ischemia Electrocardiogram demonstrating sinus rhythm with ST-segment elevation in aVR and V1 and diffuse upsloping ST-segment depressions.
Figure 2
Figure 2
Evolution of Electrocardiographic Changes Electrocardiogram demonstrating sinus rhythm with ST-segment elevation in aVR and peaked T waves in the anterior leads.
Figure 3
Figure 3
Ventricular Tachycardia Electrocardiogram demonstrating a wide-complex tachycardia with a capture beat consistent with ventricular tachycardia.
Figure 4
Figure 4
Right Adrenal Mass Computed tomography scan revealing a 5.7-cm right adrenal mass with evidence of hemorrhage (arrow).
Figure 5
Figure 5
Metaiodobenzylguanidine Accumulation in the Right Adrenal Region A total body metaiodobenzylguanidine scan demonstrating evidence of accumulation in the right adrenal region.
Figure 6
Figure 6
Histopathological Assessment of the Pheochromocytoma Histopathological assessment showing a well-circumscribed mass surrounded by a thin fibrous capsule (red arrow) (Hematoxylin and eosin staining magnification is x4).
Figure 7
Figure 7
Immunohistochemical Assessment of the Pheochromocytoma Immunohistochemical assessment demonstrating tumor cells strongly positive for the neuroendocrine marker chromogranin (Magnification is x20).
See this image and copyright information in PMC

References

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