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Case Reports
. 2023 Jan-Feb;16(1):71-73.
doi: 10.4103/apc.apc_89_22. Epub 2023 Apr 4.

Challenges to manage primary chylopericardium in children

Ishita Majumdar  1 , Hemant Kumar Nayak  2 , Rajarshi Ghosh  3 , Srirup Chatterjee  3 , Prithwish Roy  4 , Devdeep Mukherjee  5
Affiliations
Case Reports

Challenges to manage primary chylopericardium in children

Ishita Majumdar et al. Ann Pediatr Cardiol. 2023 Jan-Feb.

Abstract

Primary chylopericardium (PC) is a rare entity in the pediatric population with very few reported cases. Most cases of chylopericardium manifest after trauma or following cardiac surgery. The other etiologies which may lead to chylopericardium are malignancy, tuberculosis, or congenital lymphangiomatosis. We report two cases of PC in the pediatric population with contrasting outcomes. Both failed conservative management with dietary modification and octreotide. Surgery with pleuropericardial and pleuroperitoneal windows was performed in both. The first case had a thoracic duct ligation. The first patient died, and the second survived.

Keywords: Chylopericardium; octreotide; pericardial effusion; pericardiocentesis.

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Conflict of interest statement

There are no conflicts of interest.

Figures

Figure 1
Figure 1
(a) Chest X-ray suggestive of pericardial effusion in case 1. (b) Echocardiography suggestive of pericardial effusion in case 1. (c) HRCT thorax suggestive of pericardial effusion in case 2. (d) Normal chest X-ray for case 2 in follow-up. HRCT: High resolution computerised tomography
Figure 2
Figure 2
Flowchart for approach to a child with primary chylopericardium
See this image and copyright information in PMC

References

    1. Ossiani MH, McCauley RG, Patel HT. Primary idiopathic chylopericardium. Pediatr Radiol. 2003;33:357–9. - PubMed
    1. Courtney M, Ayyagari RR. Idiopathic chylopericardium treated by percutaneous thoracic duct embolization after failed surgical thoracic duct ligation. Pediatr Radiol. 2015;45:927–30. - PubMed
    1. Mandarry MT, Ru XH, Wei ZQ, Ge MJ. Primary idiopathic chylopericardium: A rare case with a synopsis of the literature. Singapore Med J. 2012;53:e156–8. - PubMed
    1. Sleilaty G, Rassi I, Alawi A, Jebara VA. Primary isolated chronic chylopericardium. Interact Cardiovasc Thorac Surg. 2002;1:86–7. - PubMed
    1. Yüksel M, Yildizeli B, Zonüzi F, Batirel HF. Isolated primary chylopericardium. Eur J Cardiothorac Surg. 1997;12:319–21. - PubMed

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