Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
Case Reports
. 2020 Aug 29;1(4):205-209.
doi: 10.36518/2689-0216.1077. eCollection 2020.

Flash Pulmonary Edema: A Case and Review of Left Ventricular Non-Compaction Cardiomyopathy

Paula J Watts  1   2 , Oliver S Garbo  1   2 , Wendy Barrett  1   2 , Michael Kopstein  1   2 , Ryan Maybrook  1   3 , Dmitriy Scherbak  1   2   4
Affiliations
Case Reports

Flash Pulmonary Edema: A Case and Review of Left Ventricular Non-Compaction Cardiomyopathy

Paula J Watts et al. HCA Healthc J Med. .

Abstract

Description Left ventricular non-compaction cardiomyopathy is an uncommon type of cardiomyopathy caused by malformation of the myocardium during embryogenesis. This results in trabeculations within the ventricular wall that can affect the left and, less commonly, right ventricles. Presentation ranges from clinically asymptomatic to life-threatening arrhythmias. It is a rare and relatively unknown form of cardiomyopathy, though thought to be underdiagnosed. Prevalence is increasing due to improvements in imaging and awareness. Management is similar to that of other cardiomyopathies including angiotensin-converting-enzyme inhibitors or angiotensin receptor blockers, beta-blockers, diuretics, automatic implantable cardioverter defibrillator placement and cardiac transplantation. We present a case of a 38-year-old, otherwise healthy, Indian male who presented with flash pulmonary edema and was found to have left ventricular non-compaction cardiomyopathy. This report includes a review of left ventricular non-compaction cardiomyopathy.

Keywords: LVNC; arrhythmia; cardiomyopathies/physiology/etiology/genetics; echocardiography; inborn genetic diseases; pulmonary edema/etiology; spongiform cardiomyopathy.

PubMed Disclaimer

Conflict of interest statement

Conflicts of Interest The authors declare they have no conflicts of interest.

Figures

Figure 1
Figure 1
Apical 4-chamber view demonstrating classic non-compaction cardiomyopathy appearance with prominent trabeculations and intertrabecular recesses.
Figure 2
Figure 2
Parasternal short axis view showing >2:1 ratio of non-compacted to compacted myocardium. End-systole. (Zurich criteria)
See this image and copyright information in PMC

References

    1. Arbustini E, Weidemann F, Hall JL. Left ventricular noncompaction: a distinct cardiomyopathy or a trait shared by different cardiac diseases? J Am Coll Cardiol. 2014;64(17):1840–1850. doi: 10.1016/j.jacc.2014.08.030. - DOI - PMC - PubMed
    1. Dusek J, Ostádal B, Duskova M. Postnatal persistence of spongy myocardium with embryonic blood supply. Arch Pathol. 1975;99(6):312–317. - PubMed
    1. Bennett CE, Freudenberger R. The Current Approach to Diagnosis and Management of Left Ventricular Noncompaction Cardiomyopathy: Review of the Literature. Cardiol Res Pract. 2016;2016:5172308. doi: 10.1155/2016/5172308. - DOI - PMC - PubMed
    1. Ikeda U, Minamisawa M, Koyama J. Isolated left ventricular non-compaction cardiomyopathy in adults. J Cardiol. 2015;65(2):91–97. doi: 10.1016/j.jjcc.2014.10.005. - DOI - PubMed
    1. Ackerman MJ, Priori SG, Willems S, et al. HRS/EHRA expert consensus statement on the state of genetic testing for the channelopathies and cardiomyopathies this document was developed as a partnership between the Heart Rhythm Society (HRS) and the European Heart Rhythm Association (EHRA) Heart Rhythm. 2011;8(8):1308–1339. doi: 10.1016/j.hrthm.2011.05.020. - DOI - PubMed

Publication types

LinkOut - more resources