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Case Reports
. 2023 Jan-Mar;33(1):43-48.
doi: 10.4103/jcecho.jcecho_13_23. Epub 2023 May 29.

Rapid Onset Idiopathic Pulmonary Hypertension: A Case Report with a Review of Echocardiographic Parameters

Lorenzo Pistelli  1 , Maurizio Cusmà Piccione  1 , Francesca Parisi  1 , Gianluca Di Bella  1 , Antonio Micari  1 , Giampaolo Vetta  1 , Antonio Parlavecchio  1 , Agustin Ezequiel Molinero  1 , Armando Lo Savio  1 , Concetta Zito  1
Affiliations
Case Reports

Rapid Onset Idiopathic Pulmonary Hypertension: A Case Report with a Review of Echocardiographic Parameters

Lorenzo Pistelli et al. J Cardiovasc Echogr. 2023 Jan-Mar.

Abstract

Pulmonary hypertension (PHT) is an emerging issue. The prognosis in PHT is usually poor, independently from the etiology, with progressive right ventricle failure. Despite right Heart Catheterism is the gold standard for diagnosis of PHT, echocardiography provides important information about prognosis and is helpful in both follow-up and first evaluation of PHT patients, showing a good correlation with invasively measured parameters by right heart catheterization. However, it is important to understand the limits of this method, particularly in some settings, where transthoracic echocardiography has shown a lack of accuracy. In this case report we documented a case of rapid onset (3 months) idiopathic PHT and we provided a critical analysis of echocardiographic role in PHT.

Keywords: McConnel sign; precapillary pulmonary hypertension; pulmonary hypertension; pulmonary vascular resistance; right heart failure; right ventricle.

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Conflict of interest statement

There are no conflicts of interest.

Figures

Figure 1
Figure 1
Apical four-chamber view. Right ventricular dilation seen at February’s evaluation
Figure 2
Figure 2
Parasternal short axis view
Figure 3
Figure 3
Pulmonary valve acceleration time (a) and flying W sign (b)
See this image and copyright information in PMC

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