Congenital pancreatic hypoplasia: a syndrome of exocrine and endocrine pancreatic insufficiency
- PMID: 3746536
- DOI: 10.1016/s0022-3476(86)80119-6
Congenital pancreatic hypoplasia: a syndrome of exocrine and endocrine pancreatic insufficiency
Abstract
We describe two brothers with small size at birth, early-onset insulin-dependent diabetes, and pancreatic exocrine insufficiency. In contrast to the findings in pancreatic aplasia, their serum C-peptide and glucagon levels were measurable. These findings, in concert with their clinical courses, are consistent with the diagnosis of congenital pancreatic hypoplasia.
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