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Case Reports
. 2023 Apr;15(2):133-135.
doi: 10.34172/mejdd.2023.332. Epub 2023 Apr 30.

Atypical Presentation of Adult-Onset Still's Disease

Elham Sobhrakhshankhah  1 , Farhad Zamani  1 , Behdad Behnam  1 , Hossein Ajdarkosh  1 , Amirhossein Faraji  1 , Mahmoodreza Khonsari  1 , Mehdi Nikkhah  1
Affiliations
Case Reports

Atypical Presentation of Adult-Onset Still's Disease

Elham Sobhrakhshankhah et al. Middle East J Dig Dis. 2023 Apr.

Abstract

Adult-onset Still's disease (AOSD) is a rare rheumatic disorder with various presentations. It is diagnosed based on the Yamaguchi criteria, besides the exclusion of infectious diseases and other rheumatic disorders and malignancies. Here, we describe a case of a young man, presenting with remittent fever, abdominal pain, and persistent nausea. Further evaluations showed elevated acute phase reactants, abnormal levels of liver transaminase, multiple lymphadenopathies, and pleural effusion. He was finally diagnosed with AOSD and responded well to corticosteroids and methotrexate. We describe the present case to alert gastroenterologists to AOSD as a rare differential diagnosis in patients with persistent gastrointestinal symptoms.

Keywords: Abdominal pain; Adult-onset; Persistent nausea; Still’s disease.

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Conflict of interest statement

Competing Interests The authors declare no conflict of interest related to this work.

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