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Case Reports
. 2024 Jan-Feb;40(1):e1-e4.
doi: 10.1097/IOP.0000000000002484. Epub 2023 Aug 8.

Hybrid Schwannoma-Perineurioma of the Orbit

Benjamin Zhou  1 , Tatyana Milman  2 , Fausto J Rodriguez  3 , Roger E Turbin  1 , Paul D Langer  1
Affiliations
Case Reports

Hybrid Schwannoma-Perineurioma of the Orbit

Benjamin Zhou et al. Ophthalmic Plast Reconstr Surg. 2024 Jan-Feb.

Abstract

A 52-year-old woman presented with a 6-month history of progressive right proptosis associated with intermittent right retrobulbar and facial pain. MRI revealed a heterogeneously enhancing, well-circumscribed, ovoid, soft tissue mass in the intraconal space near the right orbital apex displacing the optic nerve medially. Excisional biopsy established the diagnosis of a schwannoma-perineurioma hybrid peripheral nerve sheath tumor (HPNST). This case represents only the second reported occurrence, to our knowledge, of an orbital schwannoma-perineurioma HPNST.

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Conflict of interest statement

The authors have no financial or conflicts of interest to disclose.

References

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