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Review
. 2023 Nov;58(11):3013-3022.
doi: 10.1002/ppul.26641. Epub 2023 Aug 18.

Cystic fibrosis year in review 2022

Jeeyeon Kim  1   2 , Benjamin Lyman  1   3 , Adrienne P Savant  1   2
Affiliations
Review

Cystic fibrosis year in review 2022

Jeeyeon Kim et al. Pediatr Pulmonol. 2023 Nov.

Abstract

Remarkable medical advancements have been made for people with cystic fibrosis (CF) in recent years, with an abundance of research continuing to be conducted worldwide. With concern for limitations in access to highly effective CFTR modulators, as well as the recent Coronavirus Disease-19 pandemic, there has been a consistent effort to understand and improve CF screening, disease burden, diagnosis, and management. Our aim in this review is to present articles from 2022 with an emphasis on clinically relevant studies. We hope this will serve as a broad overview of the research published in the past year.

Keywords: CFTR modulators; cystic fibrosis; lung transplantation; newborn screening; obesity; pancreatic insufficiency; pulmonary exacerbations.

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References

REFERENCES

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    1. Rosenfeld M, Ostrenga J, Cromwell EA, et al. Real-world associations of US cystic fibrosis newborn screening programs with nutritional and pulmonary outcomes. JAMA Pediatr. 2022;176(10):990-999.
    1. McColley SA, Martiniano SL, Ren CL, et al. Disparities in first evaluation of infants with cystic fibrosis since implementation of newborn screening. J Cyst Fibros. 2023;22(1):89-97.
    1. Sontag MK, Miller JI, McKasson S, et al. Newborn screening for cystic fibrosis: aqualitative study of successes and challenges from universal screening in the United States. Int J Neonatal Screen. 2022;8(3):38.

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