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Case Reports
. 2023 Aug 1;15(8):e42797.
doi: 10.7759/cureus.42797. eCollection 2023 Aug.

Klippel-Trenaunay Syndrome Associated With Urinary Tract Hemangiomas: A Case Report

Mohammed Ramdani  1   2 , Anouar El Moudane  1 , Youness Tahri  1 , Ahmed Jdaini  1 , Achraf Benamou  1 , Mohamed Mokhtari  1 , Ali Barki  1
Affiliations
Case Reports

Klippel-Trenaunay Syndrome Associated With Urinary Tract Hemangiomas: A Case Report

Mohammed Ramdani et al. Cureus. .

Abstract

The association between Klippel-Trenauney syndrome (KTS) and bladder hemangiomas is rare. The most common clinical manifestation is hematuria. The diagnosis is made from the characteristic cystoscopic appearance of the tumor. We report the case of a patient presenting recurrent macroscopic hematuria in the context of KTS. A cystoscopic evaluation revealed bladder hemangiomas. A conservative approach consisting of bladder irrigation and close follow-up was chosen as therapy. Conservative treatment of bladder irrigation and close follow-up is the recommended initial treatment of moderate and infrequent episodes of hematuria in this context. The more invasive therapeutic options have to be considered especially for frequent or life-threatening episodes of hematuria. This case suggests that conservative treatment may be effective in treating moderate and infrequent episodes of hematuria due to bladder hemangioma in the context of KTS. Further studies are required to adequately establish the effectiveness, limitations, and complications of each approach.

Keywords: bladder hemangioma; case report; congenital; klippel trenauney syndrome; recurrent hematuria.

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Conflict of interest statement

The authors have declared that no competing interests exist.

Figures

Figure 1
Figure 1. Cutaneous hyperpigmentation with raised margins (port wine stains) over the lateral aspect of the right lower limb, associated with dilated veins
Figure 2
Figure 2. Endoscopic view of bladder angioma
See this image and copyright information in PMC

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