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Case Reports
. 2023 Sep 13;17(9):e01722.
doi: 10.1213/XAA.0000000000001722. eCollection 2023 Sep 1.

Perioperative Autonomic Dysfunction in a Patient With Charcot-Marie-Tooth Disease: A Case Report

Wissam Maroun  1 , Carol Abi Shadid  1 , Mohamed Fayed  2 , Carine Foz  1 , Jean Beresian  1 , Ahmad Oseili  1
Affiliations
Case Reports

Perioperative Autonomic Dysfunction in a Patient With Charcot-Marie-Tooth Disease: A Case Report

Wissam Maroun et al. A A Pract. .

Abstract

Autonomic dysfunction can lead to unexpected hemodynamic instability during surgery, and best practices for the perioperative care of patients with this condition are not well-defined. We report the case of a 63-year-old woman with Charcot-Marie-Tooth disease who experienced perioperative autonomic dysfunction characterized by severe fluctuations in blood pressure while under spinal anesthesia. However, <1 month later, a second hip surgery performed under general anesthesia with special precautions resulted in an uncomplicated perioperative course, with only mild fluctuations in blood pressure.

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Conflict of interest statement

The authors declare no conflicts of interest.

References

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