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Case Reports
. 2023 Sep;16(3):200-202.
doi: 10.1177/1753495X221078447. Epub 2022 Feb 11.

Pregnancy following personalised aortic root support in Marfan syndrome

Christina Coroyannakis  1 , Maite Tome  1 , Ingrid Watt-Coote  1 , Matthew Cauldwell  1
Affiliations
Case Reports

Pregnancy following personalised aortic root support in Marfan syndrome

Christina Coroyannakis et al. Obstet Med. 2023 Sep.

Abstract

Marfan syndrome (MFS) is linked with adverse pregnancy events, one of the most significant being aortic dissection. We present a case of a woman with MFS with prior aortic root dilatation who opted for a Personalised External Aortic Root Support (PEARS). To date, she is only the fifth woman to have had this valve-sparing procedure prior to pregnancy. We outline her care in a tertiary centre with multidisciplinary expertise, from preconception through to the postpartum period.

Keywords: Marfan syndrome; external aortic root support; pregnancy.

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Conflict of interest statement

The author(s) declared no potential conflicts of interest with respect to the research, authorship, and/or publication of this article.

Figures

Image 1.
Image 1.
MRI imaging showing 2-chamber-view of the PEARS in situ wrapped around the root of the aorta.
See this image and copyright information in PMC

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