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Case Reports
. 2023 Sep 16;2023(9):rjad507.
doi: 10.1093/jscr/rjad507. eCollection 2023 Sep.

Liver transplantation for polycystic liver disease: a case report

Maris Niibek  1 , Andrei Uksov  1
Affiliations
Case Reports

Liver transplantation for polycystic liver disease: a case report

Maris Niibek et al. J Surg Case Rep. .

Abstract

A 57-year-old man complained about abdominal distension and pain, constant feeling of early satiety. He was diagnosed with polycystic kidneys at the age of 24 and liver cysts discovered at the age of 38. The CT scan revealed 33 x 21 x 27 cm polycystic liver with cysts up to 7 cm in diameter. In 2009-2019 the patient was repeatedly punctured for liver cysts. Considering the continued enlargement of the liver and the worsening of complaints, the patient was put on the waiting list for a liver transplant in the spring of 2019. The patient went through liver transplantation on 11th of July 2022, the liver measures were 53 x 37 x 39 x 16 cm and weight 14,75 kg. The postoperative course was uneventful. Liver transplantation can be very effective treatment method that significantly improves the quality of life in PLD patients.

Keywords: liver; liver transplantation; polycystic liver disease; transplantation.

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Conflict of interest statement

We declare that there is no conflict of interests.

Figures

Figure 1
Figure 1
Computed tomography showed extremely enlarged liver with the dimensions of 33 x 21 x 27 cm.
Figure 2
Figure 2
Massive hepatomegaly and previous operations made mobilization of the liver very difficult.
Figure 3
Figure 3
The final pathology revealed the liver measures 53 x 37 x 39 x 16 cm and weight 14,75 kg.
See this image and copyright information in PMC

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