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Case Reports
. 2023 Sep 15:2023:5596890.
doi: 10.1155/2023/5596890. eCollection 2023.

Intravascular Large B-Cell Lymphoma

Mehdi Loukhnati  1 , Fatima Ezzahra Lahlimi  1 , Illias Tazi  1
Affiliations
Case Reports

Intravascular Large B-Cell Lymphoma

Mehdi Loukhnati et al. Case Rep Hematol. .

Abstract

Intravascular large B-cell lymphoma (IVBCL) is a very rare and aggressive subtype of extranodal diffuse large B-cell lymphoma (DLBCL) involving the growth of lymphoma cells within blood vessels of all organ types. We present the case of a 55-year-old North-African man with no prior history of neoplastic disease presenting with weight loss and an isolated splenomegaly. Investigations led to the diagnosis of this disease. To the best of our knowledge, this is the first case recorded in Africa. Through this article, we discuss this case and outline the common presentation, paraclinical investigations, and treatment options of IVBCL.

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Conflict of interest statement

The authors declare that there are no conflicts of interest.

Figures

Figure 1
Figure 1
Bone marrow biopsy: palisade arrangement of atypical cells mixed with red blood cells within the vessels.
Figure 2
Figure 2
PET scan showing bone marrow and spleen hypermetabolism.
See this image and copyright information in PMC

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