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Case Reports
. 2023 Aug 31;15(8):e44425.
doi: 10.7759/cureus.44425. eCollection 2023 Aug.

Cardiac CT Angiography-Guided Management of Giant Coronary Artery Aneurysms in Atypical Kawasaki Disease: A Case Report and Review of Literature

Affiliations
Case Reports

Cardiac CT Angiography-Guided Management of Giant Coronary Artery Aneurysms in Atypical Kawasaki Disease: A Case Report and Review of Literature

Jyothi Prakash R et al. Cureus. .

Abstract

Kawasaki disease (KD) is an auto-immune, acute febrile illness mostly affecting young children. It may develop into vasculitis characterized by coronary artery aneurysms (CAA) if not diagnosed and managed earlier. Timely diagnosis and appropriate treatment eventually avoid the risk of the development of CAA. We present the case of a 21-month-old female child with a history of persistent fever for nearly 10 days who further developed desquamations and presented for cardiac evaluation. Atypical KD with the development of giant CAAs was effectively diagnosed by cardiac computed tomographic angiography (CCTA) and was appropriately managed.

Keywords: atypical kawasaki disease; cardiac computed tomographic angiography; ccta; coronary artery aneurysm; echocardiography; intravenous immunoglobulin.

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Conflict of interest statement

The authors have declared that no competing interests exist.

Figures

Figure 1
Figure 1. Echocardiographic image showing a coronary artery aneurysm in the RCA (arrows)
RCA: right coronary artery
Figure 2
Figure 2. Comprehensive assessment of coronary artery involvement by CCTA: 3D VR image of (A) the aortic root with coronary vessels, (B) the whole heart, and (C) an outline MIP image of the heart, revealing several aneurysms in the proximal and mid-RCA (arrows and stars) and distal LMCA (arrows), and giant aneurysms in the proximal and mid-LAD (arrows and stars).
CCTA: cardiac computed tomographic angiography; 3D: three dimensional; VR: volume rendered; MIP: maximum intensity projection; RCA: right coronary artery, LMCA: left main coronary artery; LAD: left anterior descending artery

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