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Case Reports
. 2023 Oct 3;10(10):e01171.
doi: 10.14309/crj.0000000000001171. eCollection 2023 Oct.

Preoperative Nasobiliary Drainage as a Predictor of Response Before Surgical Fistula Creation in Joubert Syndrome With Refractory Cholestatic Pruritis

Maya Biermann  1 , Preeyanka Rubiana Sundar  2 , Hima Veeramachaneni  2 , Field Willingham  2
Affiliations
Case Reports

Preoperative Nasobiliary Drainage as a Predictor of Response Before Surgical Fistula Creation in Joubert Syndrome With Refractory Cholestatic Pruritis

Maya Biermann et al. ACG Case Rep J. .

Abstract

Cholestatic pruritus is a debilitating symptom associated with many liver diseases and is often refractory to medical management. Nasobiliary drainage is a relatively safe and effective method for treating intractable cholestatic pruritus. It should be considered for patients with refractory cholestatic pruritus who have failed or have contraindications to medical therapy as a predictor of response before surgical fistula creation.

Keywords: Joubert syndrome; nasobiliary drainage; pruritus.

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Figures

Figure 1.
Figure 1.
Total bile acid levels before and after nasobiliary drainage.
Figure 2.
Figure 2.
(A) Endoscopic retrograde cholangiopancreatography is used to guide placement of the nasobiliary drainage tube. (B) The nasobiliary drainage tube inserted into the gallbladder.
See this image and copyright information in PMC

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