Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
Review
. 2023 Oct 10;39(1):280.
doi: 10.1007/s00383-023-05519-6.

Diagnosis and management of congenital type D esophageal atresia

Cuizhu Feng  1   2 , Long Li  1 , Yanxia Zhang  1 , Yong Zhao  3 , Jinshi Huang  4
Affiliations
Review

Diagnosis and management of congenital type D esophageal atresia

Cuizhu Feng et al. Pediatr Surg Int. .

Abstract

This study was performed to describe the current clinical practice and outcomes of type D esophageal atresia. We retrospectively analyzed 10 patients who were diagnosed with type D esophageal atresia and underwent esophageal atresia and tracheoesophageal fistula repair in the Capital Institute of Pediatrics and Beijing Children's Hospital from January 2017 to May 2022. Ten patients include three newborns and seven non-newborns. Seven (70%) cases were misdiagnosed as type C esophageal atresia before the first operation. Three neonatal children underwent thoracoscopic distal tracheoesophageal fistula ligation and esophageal anastomosis: the proximal tracheoesophageal fistula was simultaneously repaired with thoracoscopy in one of these children, and the proximal tracheoesophageal fistula was not detected under thoracoscopy in the other two children. Among the seven non-neonatal children, one underwent repair of the proximal tracheoesophageal fistula through the chest and the other six underwent repair through the neck. Nine patients were cured, and one died of complications of severe congenital heart disease. Type D esophageal atresia lacks specific clinical manifestations. Misdiagnosis as type C esophageal atresia is the main cause of an unplanned reoperation. Patients without severe malformations have a good prognosis.

Keywords: Esophagography; Surgical treatment; Tracheoscopy; Type D esophageal atresia.

PubMed Disclaimer

Conflict of interest statement

The authors declare no competing interests.

References

    1. Pedersen RN, Calzolari E, Husby S, et al. Oesophageal atresia: prevalence, prenatal diagnosis and associated anomalies in 23 European regions. Arch Dis Child. 2012;97(3):227–232. doi: 10.1136/archdischild-2011-300597. - DOI - PubMed
    1. Oddsberg J, Lu Y, Lagergren J. Aspects of esophageal atresia in a population-based setting: incidence, mortality and cancer risk. Pediatr Surg Int. 2012;28(3):249–257. doi: 10.1007/s00383-011-3014-1. - DOI - PubMed
    1. Sfeir R, Bonnard A, Khen-Dunlop N, et al. Esophagealatresia: data from a national cohort. J Pediatr Surg. 2013;48(8):1664–1669. doi: 10.1016/j.jped-surg.2013.03.075. - DOI - PubMed
    1. Leoncini E, Bower C, Nassar N. Oesophageal atresia and tracheo-oesophageal fistula in Western Australia: prevalence and trends. J Paediatr Child Health. 2015;51(10):1023–1029. doi: 10.1111/jpc.12909. - DOI - PubMed
    1. Lloreda-Garcfa JM, Sevilla-Denia S, Leante-Castellanos JL, et al. Type IV esophageal atresia with nasogastric tube in stomach. J Neonatal Surg. 2017;6(2):44. doi: 10.21699/jns.v6i2.582. - DOI - PMC - PubMed

LinkOut - more resources