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Comment
. 2023 Nov 2;25(11):euad312.
doi: 10.1093/europace/euad312.

Arrhythmic risk stratification in arrhythmogenic right ventricular cardiomyopathy

Alessio Gasperetti  1   2   3 , Cynthia A James  1 , Richard T Carrick  1 , Alexandros Protonotarios  4 , Anneline S J M Te Riele  3 , Julia Cadrin-Tourigny  5 , Paolo Compagnucci  6 , Firat Duru  7 , Peter van Tintelen  2 , Perry M Elliot  4 , Hugh Calkins  1
Affiliations
Comment

Arrhythmic risk stratification in arrhythmogenic right ventricular cardiomyopathy

Alessio Gasperetti et al. Europace. .

Abstract

Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a heritable cardiomyopathy characterized by a predominantly arrhythmic presentation. It represents the leading cause of sudden cardiac death (SCD) among athletes and poses a significant morbidity threat in the general population. As a causative treatment for ARVC is still not available, the placement of an implantable cardioverter defibrillator represents the current cornerstone for SCD prevention in this setting. Thanks to international ARVC-dedicated efforts, significant steps have been achieved in recent years towards an individualized, patient-centred risk stratification approach. A novel risk calculator algorithm estimating the 5-year risk of arrhythmias of patients with ARVC has been introduced in clinical practice and subsequently validated. The purpose of this article is to summarize the body of evidence that has allowed the development of this tool and to discuss the best way to implement its use in the care of an individual patient.

Keywords: Arrhythmogenic right ventricular cardiomyopathy; ICD; Primary Prevention; Risk stratification.

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Conflict of interest statement

Conflict of interest: none declared.

Figures

Graphical Abstract
Graphical Abstract
Figure 1
Figure 1
Summary of current guideline indications for ICD placement in patients with ARVC.
Figure 2
Figure 2
Summary of characteristics of the ARVC risk calculator and its implementation in the clinical workflow.
Figure 3
Figure 3
Summary of the clinical pillars for the management of patients with ARVC. HF, heart failure.
See this image and copyright information in PMC

Comment on

References

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