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. 2024 Feb;59(2):492-495.
doi: 10.1002/ppul.26757. Epub 2023 Nov 17.

Persistent lobar atelectasis in an infant with cystic fibrosis: The role for flexible bronchoscopy and poractant alfa

Megan N Januska  1   2 , Elinor Langfelder-Schwind  3 , Alfin G Vicencio  1 , Maria N Berdella  3   4
Affiliations

Persistent lobar atelectasis in an infant with cystic fibrosis: The role for flexible bronchoscopy and poractant alfa

Megan N Januska et al. Pediatr Pulmonol. 2024 Feb.
No abstract available

Keywords: CFTR modulator therapy; W496R; case report; interventional bronchoscopy; surfactant.

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Conflict of interest statement

Conflict of Interest Statement: The authors declare no conflict of interest.

Figures

Figure 1.
Figure 1.
A) Initial CXR demonstrating RUL atelectasis during an acute viral illness at three months of age, B) follow-up CXR demonstrating persistent RUL atelectasis at five months of age following flexible bronchoscopy with the instillation of rhDNase and concomitant air insufflation, C) follow-up CXR demonstrating improved RUL atelectasis at eight months of age following flexible bronchoscopy with the instillation of poractant alpha and concomitant air insufflation and the initiation of ivacaftor, and D) follow-up CXR demonstrating nearly resolved RUL atelectasis at eleven months of age following flexible bronchoscopy with the instillation of poractant alpha and concomitant air insufflation.
Figure 2.
Figure 2.
Chest CT demonstrating segmental RUL atelectasis, primarily involving the posterior segment, at nine months of age; axial images progress in the cranial (A) to caudal (D) direction.
See this image and copyright information in PMC

References

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