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Case Reports
. 2023 Oct 22;15(10):e47453.
doi: 10.7759/cureus.47453. eCollection 2023 Oct.

A Curious Case of Proptosis and Intracranial Calcifications Caused by a Vein of Galen Aneurysmal Malformation

Sandra C M  1 , Breman A Peethambar  2
Affiliations
Case Reports

A Curious Case of Proptosis and Intracranial Calcifications Caused by a Vein of Galen Aneurysmal Malformation

Sandra C M et al. Cureus. .

Abstract

Vein of Galen aneurysmal malformation (VGAM) is a rare, congenital, intracerebral arteriovenous malformation with a poor prognosis. This disorder commonly presents during the neonatal period and rarely in infancy and childhood. Reported here is a case of VGAM in a three-month-old female baby who presented with proptosis and intracranial calcifications, which are rare presentations of this rare entity. The diagnosis was confirmed by magnetic resonance imaging (MRI).

Keywords: cardiac failure; digital subtraction angiography; intracranial calcifications; proptosis; vein of galen.

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Conflict of interest statement

The authors have declared that no competing interests exist.

Figures

Figure 1
Figure 1. Axial CT images of the brain showed linear hyperdensities in the subcortical white matter of bilateral parietal lobes (red arrow) and periventricular regions (yellow arrow) suggestive of intracranial calcifications. Ventricles appeared mildly dilated. Increased subarachnoid space was noted in bilateral frontoparietal regions suggestive of benign enlargement of the subarachnoid space in infancy.
Figure 2
Figure 2. Sagittal (2a), coronal (2b), and axial (2c) 1.5T MR images of the abdomen showed a characteristic appearance of VGAM with a large flow void in the midline, posterior to third ventricle representing enlarged median prosencephalic vein of Markowski of maximum diameter 7 mm (green arrows). Arterial feeders were seen along the anterior wall of the vein (blue arrows).
Figure 3
Figure 3. Sagittal (3a and 3c) and axial (3b) T2-weighted MR images showed dilatation of the straight sinus (3a), left transverse sinus (3b), and left sigmoid sinus (3c)
Figure 4
Figure 4. Axial (4a, 4b, and 4c) T2-weighted MR images showed dilatation of the left superior petrosal sinus (4a) and left superior ophthalmic vein (4b and 4c)
Figure 5
Figure 5. Susceptibility-weighted image (SWI) showed multiple, tiny blooming areas in periventricular regions, which concurred with the calcifications previously seen on CT
See this image and copyright information in PMC

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