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. 2023 Dec;5(6):e230138.
doi: 10.1148/ryct.230138.

Corkscrew Mesenteric Arteries and Tortuous Descending Aorta in Autosomal Recessive Cutis Laxa

Jayakrishnan Radhakrishnan  1 , Jineesh Valakkada  1 , Anoop Ayyappan  1 , Pavan Kumar Bellala  1
Affiliations

Corkscrew Mesenteric Arteries and Tortuous Descending Aorta in Autosomal Recessive Cutis Laxa

Jayakrishnan Radhakrishnan et al. Radiol Cardiothorac Imaging. 2023 Dec.
No abstract available

Keywords: Aneurysms; Arteries; Connective Tissue Disorders; Vascular.

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Conflict of interest statement

Disclosures of conflicts of interest: J.R. No relevant relationships. J.V. No relevant relationships. A.A. No relevant relationships. P.K.B. No relevant relationships.

Figures

Clinical images of an 8-year-old male patient with autosomal recessive cutis laxa show (A) joint hyperextensibility and (B) skin laxity.
Figure 1:
Clinical images of an 8-year-old male patient with autosomal recessive cutis laxa show (A) joint hyperextensibility and (B) skin laxity.
Volume-rendered CT images in the patient show (A) an ascending aortic aneurysm with (B) severe tortuosity of the descending aorta. (C) Coronal maximum intensity projection image shows severe tortuosity and corkscrew appearance of the branches of the superior mesenteric artery (yellow arrow).
Figure 2:
Volume-rendered CT images in the patient show (A) an ascending aortic aneurysm with (B) severe tortuosity of the descending aorta. (C) Coronal maximum intensity projection image shows severe tortuosity and corkscrew appearance of the branches of the superior mesenteric artery (yellow arrow).
See this image and copyright information in PMC

References

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Supplementary concepts

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