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Case Reports
. 2024 Jan 14:49:102336.
doi: 10.1016/j.jcot.2024.102336. eCollection 2024 Feb.

Pierre Robin sequence coexisting with ectopic kidney, bilateral developmental hip dysplasia in a child - A rare case report

Eshaan Mishra  1 , Rajesh Rana  1 , Sarthak Sahoo  1
Affiliations
Case Reports

Pierre Robin sequence coexisting with ectopic kidney, bilateral developmental hip dysplasia in a child - A rare case report

Eshaan Mishra et al. J Clin Orthop Trauma. .

Erratum in

Abstract

Pierre Robin sequence is a rare congenital disorder with variable associations. A two-year-old female child was brought in with complaints of an abnormal gait and right lower limb shortening. A comprehensive clinical evaluation unveiled facial characteristics resembling those of Pierre Robin Sequence, including micrognathia, a cleft palate, and glossoptosis. The child also exhibited retrognathia, a low posterior hairline, bilateral developmental dysplasia of the hips, right foot syndactyly, and a left ectopic kidney as confirmed by ultrasonography. Radiological examination showed bilateral developmental dysplastic hips. The connection between Pierre Robin sequence and the presence of bilateral dysplastic hips and an ectopic kidney is an unusual and rare combination.

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Conflict of interest statement

The authors declare that they have no known competing financial interests or personal relationships that could have appeared to influence the work reported in this paper.

Figures

Fig. 1
Fig. 1
Clinical pictures showing cleft palate & Micrognathia.
Fig. 2
Fig. 2
Pre operative radiograph of both hip.
Fig. 3
Fig. 3
CT scan of both hips showing dysplasia of hip with dislocation.
Fig. 4
Fig. 4
Intraoperative pictures showing approach, thickened elongated ligamentum teres,Varus derotation osteotomy of proximal femur,Pemberton osteotomy.
Fig. 5
Fig. 5
Post operative radiograph.
See this image and copyright information in PMC

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