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Case Reports
. 2024 Jan 17;10(2):101401.
doi: 10.1016/j.jvscit.2023.101401. eCollection 2024 Apr.

Iliac artery aneurysm endoleak management in a patient with vascular Ehlers-Danlos syndrome

Mitri K Khoury  1 , Matthew J Eagleton  1
Affiliations
Case Reports

Iliac artery aneurysm endoleak management in a patient with vascular Ehlers-Danlos syndrome

Mitri K Khoury et al. J Vasc Surg Cases Innov Tech. .

Abstract

Endovascular repair has traditionally been avoided in patients with connective tissue disorders. We describe successful treatment of multiple endoleaks of an expanding common iliac artery aneurysm previously treated with an endograft in a patient with vascular Ehlers-Danlos syndrome. The modalities used to treat the endoleaks were transgluteal embolization of the internal iliac artery and proximal and distal extension of the prior endograft. This case demonstrates endovascular management of endoleaks in patients with vascular Ehlers-Danlos syndrome can be safe and feasible.

Keywords: Connective tissue; Ehlers Danlos; Endoleak; Iliac aneurysm; Transgluteal.

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Conflict of interest statement

None.

Figures

Fig 1
Fig 1
Computed tomography angiography (CTA) demonstrating successful iliac aneurysm repair with a stent graft by an outside hospital.
Fig 2
Fig 2
Computed tomography angiography (CTA) demonstrating an endoleak around the iliac aneurysm sac (A) and patent bilateral internal iliac arteries (IIAs; B).
Fig 3
Fig 3
Left internal iliac artery (IIA) access and embolization via a transgluteal approach. A, Angiogram demonstrating the catheter within the internal iliac artery (IIA). B, Digital subtraction angiography demonstrating both a type Ib and a type II endoleak. C, Successful coiling of the IIA.
Fig 4
Fig 4
Angiography demonstrating a type Ib endoleak (A) and successful treatment with a stent graft (B).
See this image and copyright information in PMC

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