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Review
. 2024 Feb 23;16(5):897.
doi: 10.3390/cancers16050897.

Treatment of Undifferentiated Embryonal Sarcoma of the Liver in Children

Wen-Ya Lin  1 , Kang-Hsi Wu  2   3 , Chun-Yu Chen  4   5 , Bei-Cyuan Guo  6 , Yu-Jun Chang  7 , Mao-Jen Lin  8   9 , Han-Ping Wu  10   11
Affiliations
Review

Treatment of Undifferentiated Embryonal Sarcoma of the Liver in Children

Wen-Ya Lin et al. Cancers (Basel). .

Abstract

Undifferentiated embryonal sarcoma of the liver is a rare mesenchymal tumor with a highly malignant potential. It occurs almost exclusively in the pediatric population and typically has a poor outcome. Although previous studies have reported dismal prognoses, recent advances in combined treatment modalities, e.g., surgery and chemotherapy, have given cause for optimism. Even in those diseases not amenable to complete surgical resection or refractory diseases, other treatment modalities, such as liver transplant, have yielded promising results. This paper provides a review of the current treatment modalities for hepatic undifferentiated embryonal sarcoma in children.

Keywords: children; hepatic tumors; undifferentiated embryonal sarcoma.

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Conflict of interest statement

The authors declare no conflicts of interest.

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