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Case Reports
. 2024 Mar 21;12(3):e8704.
doi: 10.1002/ccr3.8704. eCollection 2024 Mar.

Interdisciplinary full mouth rehabilitation of a patient with amelogenesis imperfecta from childhood to young adult-hood: A 12-year case report

Affiliations
Case Reports

Interdisciplinary full mouth rehabilitation of a patient with amelogenesis imperfecta from childhood to young adult-hood: A 12-year case report

Élisa Caussin et al. Clin Case Rep. .

Abstract

Treatment of patients with amelogenesis imperfecta extends over many years, from childhood to early adulthood. Their management at any age is complex and has to be adapted in relation to therapies validated in the general population.

Keywords: CAD‐CAM; amelogenesis imperfecta; dentistry; full‐mouth rehabilitation; prosthodontics; rare disease.

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Conflict of interest statement

The authors declare no conflict of interest.

Figures

FIGURE 1
FIGURE 1
First consult, intraoral view of maximal intercuspal occlusion (A); composite bonding with strip crowns (B); orthopedic interception with tongue positioner (C), 2011.
FIGURE 2
FIGURE 2
Orthopantomogram, first consult at the Hospital in 2011. Enamel is less opaque than the dentin. Tooth 23 is impacted. Several malpositions are observed.
FIGURE 3
FIGURE 3
Before orthodontic treatment. Intraoral view of maximal intercuspal occlusion, overbite and tongue thrust (A); after orthodontic treatment (B).
FIGURE 4
FIGURE 4
First consult with the restorative dentistry team. Extraoral front view at rest (A); extraoral front view with natural smile (B); extraoral profile view with natural smile (C); intraoral mandibular view with SSCs on molars and composite resin on other teeth (D); maxillary view (E); intraoral left profile view, overjet increased by 4 mm, normal overbite and reduced crown height in the posterior region, Class II occlusion (F); intraoral right profile view, class II occlusion (G).
FIGURE 5
FIGURE 5
Radiographic examination. Maladjusted crowns, impacted canine (23) and endodontic treatment on tooth 12 are observed.
FIGURE 6
FIGURE 6
Teeth preparation and temporary crowns. Initial situation Sector 3 (A); minimally invasive chamfer homothetic peripheral preparations (B); temporary restorations in PMMA at increased VDO (C).
FIGURE 7
FIGURE 7
Definitive crowns milled out of zirconia (4Y‐TZP /5Y‐TZP, Emax ZirCAD MT, Ivoclar Vivadent), Sectors 2 and 3.
FIGURE 8
FIGURE 8
One month follow‐up. Extraoral front zoom view with natural harmonious smile (A); intraoral view in maximal intercuspal position (B); maxillary occlusal view (C); mandibular occlusal view (D).
FIGURE 9
FIGURE 9
3D‐printed rigid bruxism splint (KeySplint Soft®, Keystone industries) for the mandible, occlusal view with occlusal contacts marked.
FIGURE 10
FIGURE 10
Two‐year follow‐up. Extraoral front view with natural smile (A) extra‐oral front view with forced smile still not exposing the anterior cervical line (B).
FIGURE 11
FIGURE 11
Two‐year follow‐up. Extraoral front zoom view with natural harmonious smile.
FIGURE 12
FIGURE 12
Two‐year follow‐up. Intraoral right profile view (A); intraoral view in maximal intercuspal position (B); intraoral left profile view (C).
FIGURE 13
FIGURE 13
2‐year follow‐up. Maxillary occlusal view (A); mandibular occlusal view (B).

References

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