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Case Reports
. 2024 Mar-Apr;29(2):171-173.
doi: 10.4103/jiaps.jiaps_175_23. Epub 2024 Mar 4.

Penile Epithelioid Hemangioendothelioma in a Child

Palak Singhai  1 , Nitin James Peters  1 , Aravind Sekar  2 , Girdhar S Bora  3 , Ujjwal Gorsi  4 , Jai Kumar Mahajan  1
Affiliations
Case Reports

Penile Epithelioid Hemangioendothelioma in a Child

Palak Singhai et al. J Indian Assoc Pediatr Surg. 2024 Mar-Apr.

Abstract

An 8-year-old boy initially thought to have a penile arteriovenous malformation was later diagnosed with a rare vascular sarcoma, epithelioid hemangioendothelioma (EHE). Despite challenges in diagnosis, he underwent supraselective angioembolization and partial penectomy for oncological clearance. EHE, a low-grade malignancy, requires prompt identification and treatment due to potential systemic involvement.

Keywords: Epithelioid hemangioendothelioma; Pediatric penile tumor; induced hypospadias; penectomy.

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Conflict of interest statement

There are no conflicts of interest.

Figures

Figure 1
Figure 1
(a) Penile epithelioid hemangioendothelioma involving the glans penis and distal two-third of the shaft of the penis. (b) Resected specimen of penile epithelioid hemangioendothelioma postmodified partial penectomy. (c) Mid-penile neomeatus postmodified partial penectomy in a case of penile epithelioid hemangioendothelioma
Figure 2
Figure 2
(a) T2-weighted sagittal MRI showing penile epithelioid hemangioendothelioma involving the glans penis and the corpus spongiosum of distal and mid-penile shaft. (b) Selective right internal pudendal artery angiogram showing abnormal hypervascular tumor blush. Note made of coils placed during earlier embolization. (c) Postembolization, complete disappearance of tumor blush. (d) Hematoxylin and eosin stain in a case of penile epithelioid hemangioendothelioma showing oval to epithelioid cells with coarse chromatin and moderate cytoplasm, arranged in cords, sheets, and short fascicles in a mildly myxoid stroma
See this image and copyright information in PMC

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