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Review
. 2024 Aug;40(8):2599-2602.
doi: 10.1007/s00381-024-06410-y. Epub 2024 Apr 22.

Dural sinus malformation presenting with proptosis: report and review of a rare entity

Tejus M N Rao  1 , Sumit Thakar  2 , Paritosh Pandey  3 , Saritha Aryan  1
Affiliations
Review

Dural sinus malformation presenting with proptosis: report and review of a rare entity

Tejus M N Rao et al. Childs Nerv Syst. 2024 Aug.

Abstract

Dural sinus malformation (DSM) is a rare vascular malformation characterized by the dilatation of a dural venous sinus with or without an anomalous jugular bulb. Its presentation with venous-reflux-related secondary proptosis is anecdotal, with only six such cases reported so far. We report a 17-month-old boy who presented with a progressive proptosis of the right eye secondary to a DSM of the transverse sinus and torcula. Following endovascular embolization of the arterio-venous fistula, complete thrombosis of the venous lake and improvement in proptosis was noted at 6-month follow-up. Prognosis of this rare malformation is variable and dependent on specific angio-architectural features.

Keywords: Arterio-venous shunt; Dural sinus malformation; Proptosis.

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References

    1. Barbosa M, Mahadevan J, Weon YC, Yoshida Y, Ozanne A, Rodesch G, Alvarez H, Lasjaunias P (2003) Dural sinus malformations (DSM) with giant lakes, in neonates and infants: review of 30 consecutive cases. Interv Neuroradiol 9:407–424 - DOI - PubMed
    1. Lasjaunias P, Magufis G, Goulão A, Piske R, Suthipongchai S, Rodesch R, Alvarez H (1996) Anatomoclinical aspects of dural arteriovenous shunts in children: review of 29 cases. Interv Neuroradiol 2:179–191 - DOI - PubMed
    1. Okudera T, Pen Huang Y (1996) Developmental radiology of the posterior fossa dural sinuses in the human fetus: with special references to physiological enlargement of transverse and occipital sinuses, formation of emissary veins and development of superior jugular bulb from jugular sinuses. Surgery of the Intracranial Venous System 192–203
    1. Requejo F, Tcherbbis V, Gonzalez ML, Argañaraz R, Marelli JM, Mantese B (2020) Dural sinus malformation with giant pouch (DSMGP): symptoms and treatment. Child’s Nerv Syst 36:343–348 - DOI
    1. Liby P, Lomachinsky V, Petrak B, Kyncl M, Charvat F, Padr R, Tichy M (2020) Torcular dural sinus malformations: a single-center case series and a review of literature. Child’s Nerv Syst 36:333–341 - DOI

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