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Review
. 2024 Aug;40(8):2599-2602.
doi: 10.1007/s00381-024-06410-y. Epub 2024 Apr 22.

Dural sinus malformation presenting with proptosis: report and review of a rare entity

Tejus M N Rao  1 , Sumit Thakar  2 , Paritosh Pandey  3 , Saritha Aryan  1
Affiliations
Review

Dural sinus malformation presenting with proptosis: report and review of a rare entity

Tejus M N Rao et al. Childs Nerv Syst. 2024 Aug.

Abstract

Dural sinus malformation (DSM) is a rare vascular malformation characterized by the dilatation of a dural venous sinus with or without an anomalous jugular bulb. Its presentation with venous-reflux-related secondary proptosis is anecdotal, with only six such cases reported so far. We report a 17-month-old boy who presented with a progressive proptosis of the right eye secondary to a DSM of the transverse sinus and torcula. Following endovascular embolization of the arterio-venous fistula, complete thrombosis of the venous lake and improvement in proptosis was noted at 6-month follow-up. Prognosis of this rare malformation is variable and dependent on specific angio-architectural features.

Keywords: Arterio-venous shunt; Dural sinus malformation; Proptosis.

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References

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