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Review
. 2024 May 3;64(1):35.
doi: 10.1186/s42358-024-00374-y.

IgG4-related disease-rare but you should not forget it

Frederico Augusto Gurgel Pinheiro  1   2 , Ivanio Alves Pereira  3 , Alexandre Wagner Silva de Souza  4 , Henrique Ayres Mayrink Giardini  5 , Rafael Alves Cordeiro  5
Affiliations
Review

IgG4-related disease-rare but you should not forget it

Frederico Augusto Gurgel Pinheiro et al. Adv Rheumatol. .

Abstract

Immunoglobulin G4-related disease is a systemic immune-mediated disease with insidious evolution characterized by fibroinflammatory lesions over virtually any organ system. Despite the remarkable progression of knowledge, its etiology remains undefined. Due to its relapse-remitting pattern, it could accumulate irreversible damage, increasing comorbidities and mortality. This paper emphasizes key concepts for diagnosing and treating patients with this condition.

Keywords: Chronic relapsing-remitting inflammatory condition; Fibroinflammatory disease; IgG4-RD; Immunoglobulin G4-related disease; Rare diseases; Review; Rheumatic diseases.

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References

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