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Case Reports
. 2024 May 13;24(1):210.
doi: 10.1186/s12886-024-03457-y.

Lens subluxation combined with parry-romberg syndrome: case report

Yating Tang  1   2   3 , Qinghe Jing  1   2   3 , Yongxiang Jiang  4   5   6 , Yi Lu  7   8   9
Affiliations
Case Reports

Lens subluxation combined with parry-romberg syndrome: case report

Yating Tang et al. BMC Ophthalmol. .

Abstract

Background: Parry-Romberg syndrome (PRS) is a rare progressive degenerative disorder of unknown etiology. Here we report a rare case of PRS combined with lens subluxation in Eye and ENT hospital of Fudan University, Shanghai. To our knowledge, it is the first reported case of PRS combined with lens subluxation that has been managed surgically with phacoemulsification and CTR placement and IOL implantation in Shanghai.

Case presentation: A 60-year-old woman was referred for "right visual blur for 2 years" and had persistent right facial paralysis of unknown etiology since the age 12. She had right facial muscle atrophy and paralysis. Eye examination also showed the right eyelid pseudoptosis, enophthalmos, age-related cataract combined with lens subluxation existed in the right eye. The patient was diagnosed as age-related cataract and lens subluxation in the right eye and progressive hemifacial atrophy (Parry-Romberg syndrome). We conducted a combined phacoemulsification, IOL and CTR implantation and pupilloplasty surgery for the patient under general anesthesia and the postoperative UCVA was 20/30 and remained for 1 year's follow up.

Conclusions: Here we reported a rare case of PHA combined with lens subluxation in China. After appropriate eye surgery, the patient achieved satisfying vision result in the right eye.

Keywords: Cataract; Lens subluxation; PHA; Parry-romberg syndrome; Progressive hemifacial atrophy.

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Conflict of interest statement

The authors declare no competing interests.

Figures

Fig. 1
Fig. 1
A. Right facial muscle atrophy with right facial paralysis. B. Slit lamp photo of the right eye preoperatively. C. Fundus photo and OCT of the right eye. D. Slit lamp photo of the right eye postoperatively
See this image and copyright information in PMC

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