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Review
. 2024 Jun;15(2):409-413.
doi: 10.1007/s13193-024-01921-1. Epub 2024 Mar 11.

Askin's Tumor in the Chest Wall-a Rare Clinical Entity and Review of Literature

Manish Sahni  1 , Shefali Goyal  2 , Sanjeev Devgarha  2 , Anula Sisodiya  2
Affiliations
Review

Askin's Tumor in the Chest Wall-a Rare Clinical Entity and Review of Literature

Manish Sahni et al. Indian J Surg Oncol. 2024 Jun.

Abstract

Askin tumors are the rare malignancy of neuroectodermal origin of the thoracic wall. Its prevalence is more in younger age group who present with vague symptoms leading to delayed diagnosis. We hereby present a case report of complex management of large chest wall tumor in a young boy and review the literature of this entity.

Keywords: IHC (immunohistochemistry); NACT (neoadjuvant chemotherapy); OS (overall survival); POD (postoperative day); SE/PPNETS (Ewing’s sarcoma/peripheral primitive neuroectodermal tumor); SUV (standard uptake value).

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Conflict of interest statement

Conflict of InterestThe authors declare no competing interests.

Figures

Fig. 1
Fig. 1
A Clinical picture of right chest wall tumor. B Chest X ray showing right sided homogenous opacity. C CT scan chest depicting chest wall tumor with intrathoracic extension
Fig. 2
Fig. 2
A Intraoperative picture of chest wall tumor. 2 B Intrathoracic extension of tumor to upper and middle lobe of right lung. C Chest wall reconstruction with prolene mesh. D Mesh cover with Pectoralis major muscle and soft tissue with skin closure. E Postoperative healed wound
Fig. 3
Fig. 3
A Gross specimen of chest wall tumor. B Microscopic appearance -small round cell tumor cells. C IHC marker with CD 99 positive tumor cells
See this image and copyright information in PMC

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References

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