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Case Reports
. 2023 Jan;19(1):61-64.
doi: 10.48305/arya.2022.11722.2343.

Management of Patients with Vascular Ehlers-Danlos Syndrome and Acute Coronary Syndrome: a Case Report

Ilenia Alessandra Di Liberto  1 , Gerlando Pilato  1 , Giuseppe Caramanno  1
Affiliations
Case Reports

Management of Patients with Vascular Ehlers-Danlos Syndrome and Acute Coronary Syndrome: a Case Report

Ilenia Alessandra Di Liberto et al. ARYA Atheroscler. 2023 Jan.

Abstract

Background: Ehlers-Danlos syndrome (EDS) is a hereditary collagen vascular disorder characterized by joint hypermobility, skin hyperextensibility, and tissue fragility. Vascular EDS (vEDS) is a subtype of EDS which is characterized by vascular fragility.

Case presentation: This is a case report of a young man with vEDS hospitalized for myocardial infarction. He was presented with a coronary dissection and developed aortic dissection, coronary rupture, and cardiac tamponade until death.

Conclusion: This case report highlights how patients with vEDS and acute coronary syndrome show a higher risk of vascular complications compared with other patients, and their admission to the institution with a cardiac surgery room could be helpful and safe for better management of the complications. Non-invasive methods could be useful to exclude other vascular diseases, before the emergency coronary intervention.

Keywords: Acute coronary syndrome; Aortic dissection; Cardiac tamponade; Coronary dissection; Coronary rupture; Vascular Ehlers-Danlos syndrome.

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Figures

Figure 1
Figure 1
The 12-lead electrocardiography shows ST-segment elevation in the anterolateral leads
See this image and copyright information in PMC

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