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Review
. 2024 Jun;43(2):48-56.
doi: 10.36185/2532-1900-553.

Indications and techniques of non-invasive ventilation (NIV) in neuromuscular diseases

Anna Annunziata  1 , Antonietta Coppola  1 , Francesca Simioli  1 , Lidia Atripaldi  1 , Antonella Marotta  1 , Antonio Esquinas  2 , Giuseppe Fiorentino  1
Affiliations
Review

Indications and techniques of non-invasive ventilation (NIV) in neuromuscular diseases

Anna Annunziata et al. Acta Myol. 2024 Jun.

Abstract

The neuromuscular patients may experience the need for respiratory support due to the onset of respiratory failure. Some skills are essential to achieve therapeutic success. In addition to technical knowledge, it is essential to have knowledge relating to individual neuromuscular diseases. The availability of alternative respiratory supports and various interfaces can be a valuable weapon at different moments in the course of the neuromuscular disease. Furthermore, the doctor-patient relationship plays a key role as does taking care of the patient's psychological sphere.

Keywords: neuromuscolar diseases; non-invasive ventilation; respiratory failure.

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Conflict of interest statement

The authors declare no conflict of interest

Figures

Figure 1.
Figure 1.
A DMD patient, intolerant to positive pressure ventilation, treated with NPV during acute respiratory failure due to pneumonia.
Figure 2.
Figure 2.
A LGMD patient during the IAPV study. The blue arrow indicates the elastic inflatable bladder that compresses the abdomen to cause exhalation.
Figure 3.
Figure 3.
A LGMD patient affected by acute respiratory failure due to pneumococcal pneumonia, treated with HFNC and NPV.
Figure 4.
Figure 4.
Ulcer of the bridge of the nose in an ALS patient in treatment with NIV 24 hours a day. The same patient in a full-face mask.
Figure 6.
Figure 6.
Cloth nose-mouth interface.
Figure 5.
Figure 5.
Interface without pressure on the nose bridge.
See this image and copyright information in PMC

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