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Review
. 2024:1448:323-353.
doi: 10.1007/978-3-031-59815-9_23.

Cytokine Storm Syndrome Associated with Systemic Juvenile Idiopathic Arthritis

Sebastiaan J Vastert  1 , Susan P Canny  2 , Scott W Canna  3 , Rayfel Schneider  4 , Elizabeth D Mellins  5   6
Affiliations
Review

Cytokine Storm Syndrome Associated with Systemic Juvenile Idiopathic Arthritis

Sebastiaan J Vastert et al. Adv Exp Med Biol. 2024.

Abstract

The cytokine storm syndrome (CSS) associated with systemic juvenile idiopathic arthritis (sJIA) has widely been referred to as macrophage activation syndrome (MAS). In this chapter, we use the term sJIA-associated CSS (sJIA-CSS) when referring to this syndrome and use the term MAS when referencing publications that specifically report on sJIA-associated MAS.

Keywords: Interleukin-1; Interleukin-18; Interleukin-6; Macrophage activation syndrome; Systemic juvenile idiopathic arthritis.

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References

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