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Case Reports
. 2024 Aug;38(8):755-757.
doi: 10.13201/j.issn.2096-7993.2024.08.016.

[Infraglottic portion Rosai-Dorfman disease: a case report]

[Article in Chinese]
Affiliations
Case Reports

[Infraglottic portion Rosai-Dorfman disease: a case report]

[Article in Chinese]
Chenhao Hu et al. Lin Chuang Er Bi Yan Hou Tou Jing Wai Ke Za Zhi. 2024 Aug.

Abstract

Rosai Dorfman disease is a rare non Langerhans histiocytic disease with intranodal and/or extranodal manifestations, most commonly affecting cervical lymph nodes. There is no treatment guideline for this disease. This paper reports a case of infraglottic portion, which did not show typical symptoms, such as fever or lymphadenopathy, and was easily misdiagnosed as malignant tumor preoperatively. The patient underwent low-temperature plasma minimally invasive surgery combined with hormone therapy and achieved good clinical effect. By reviewing the literature, we can better understand the clinical manifestations, diagnosis and treatment of this rare disease.

摘要: Rosai-Dorfman病是一种罕见的非朗格汉斯组织细胞疾病,具有淋巴结内和(或)结外表现。目前尚无治疗这种疾病的指导方案。本文报道1例声门下区的病例,患者未表现出典型的症状,如发烧或淋巴结病,术前极易被误诊为恶性肿瘤。患者接受了低温等离子微创手术联合激素治疗,获得良好疗效。本文通过对Rosai-Dorfman病相关文献进行回顾,以便更好地了解此种罕见疾病的临床表现、诊断和治疗。.

Keywords: Rosai-Dorfman disease; subglottic diseases; surgical operation.

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Conflict of interest statement

The authors of this article and the planning committee members and staff have no relevant financial relationships with commercial interests to disclose.

Figures

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图 1
术前喉镜检查
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喉部CT检查
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图 3
喉部MR检查
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图 4
病理学检查
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图 5
术后2周喉镜检查
图 6
图 6
术后6个月喉镜检查

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