Aplasia cutis congenita of the trunk in a newborn: a rare case report
- PMID: 39315062
- PMCID: PMC11419577
- DOI: 10.11604/pamj.2024.48.52.43784
Aplasia cutis congenita of the trunk in a newborn: a rare case report
Abstract
Aplasia cutis congenita (ACC) is a rare congenital disorder defined as a congenital skin defect, characterized by the absence of all skin layers at birth. The most frequent presentation is a small erythematous ulcerated or scar-like alopecic ectodermal lesion on the scalp vertex. However, extensive cutis aplasia of the trunk is extremely uncommon. Clinical and radiological evaluation defined the appropriate treatment. We herein report a rare case of a large aplasia cutis congenita of the trunk occurring in a male newborn managed with sulfadiazine silver 1% dressing, complete healing was achieved in about a month. The report highlights that conservative treatment is a highly effective and practical option for managing non-scalp extensive ACC.
Keywords: Skin defect; aplasia cutis congenita; case report; newborn; trunk.
Copyright: El Mouloua Ahmed et al.
Conflict of interest statement
The authors declare no competing interests.
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