doi: 10.1016/j.jaad.2024.09.029.
Epub 2024 Sep 27.
Dupilumab in atopic-dermatitis-like eczema associated with inborn errors of immunity: A nationwide study
Claire Guillemin
1
, Nathalia Bellon
1
, Marie Jachiet
2
, Sébastien Barbarot
3
, Emmanuelle Bourrat
4
, Christine Chiaverini
5
, Pierre Cougoul
6
, Mikaël Ebbo
7
, Mathilde Herber
8
, Thomas Hubiche
5
, Stéphanie Mallet
9
, Marie Tauber
10
, Vivien Béziat
11
, Martin Castelle
12
, Aurélie Du Thanh
13
, Johathan Farhi
14
, Claire Fieschi
15
, Benjamin Fournier
16
, Clément Gourguechon
17
, Tamazoust Guiddir
18
, Dan Lipsker
19
, Nadia Raison-Peyron
13
, Nicolas Garcelon
20
, Morgane Cheminant
21
, Felipe Suarez
21
, Olivier Hermine
21
, Stéphane Blanche
22
, Despina Moshous
16
, Nizar Mahlaoui
12
, Benedicte Neven
16
, Christine Bodemer
23
, Romain Lévy
24
, Laura Polivka
25
; Groupe de Recherche de la Société Française de Dermatologie Pédiatrique (GR SFDP); French Atopic Dermatitis Network from the Groupe de Recherche sur l’Eczéma Atopique (GREAT)
Affiliations
Affiliations
- 1 Department of Dermatology, Reference Center for Genodermatoses (MAGEC), Necker Hospital for Sick Children, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris Cité University, Paris, France.
- 2 Department of Dermatology, Saint-Louis Hospital, AP-HP, Paris Cité University, Paris, France.
- 3 Department of Dermatology, Nantes University, CHU Nantes, INRAE, UMR 1280, PhAN, Nantes, France.
- 4 Department of Dermatology, Reference Center for Genodermatoses (MAGEC), Saint Louis Hospital, AP-HP, Paris Cité University, Paris, France.
- 5 Department of Dermatology, Reference Center for Rare Dermatological Diseases (CRMRD), Nice Center University, Nice, France.
- 6 Department of Internal Medicine, Toulouse University Cancer Institute (IUCT) Oncopole, Toulouse, France.
- 7 Department of Internal Medicine, La Timone Hospital, Aix-Marseille University, Assistance Publique -Hôpitaux de Marseille (AP-HM), Marseille, France.
- 8 Department of Internal Medicine, Strasbourg Centre University, Strasbourg, France.
- 9 Department of Dermatology, La Timone Hospital, Aix-Marseille University, AP-HM, Marseille, France.
- 10 Department of Allergology and Clinical Immunology, HCL, Lyon Sud Center University, CIRI Inserm U1111, Lyon, France.
- 11 Laboratory of Human Genetics of Infectious Diseases, Necker Branch, INSERM, Necker Hospital for Sick Children, Paris Cité University, Paris, France; Imagine Institute, INSERM UMR1163, Paris Cité University, Paris, France.
- 12 French National Reference Center for Primary Immunodeficiencies (CEREDIH), Necker Hospital for Sick Children, AP-HP, Paris, France; Pediatric Immunology-Hematology and Rheumatology Unit, Necker Hospital for Sick Children, AP-HP, Paris Cité University, Paris, France.
- 13 Department of Dermatology, Montpellier Center University, Paris, France.
- 14 Department of Hematology, Angers Center University, Angers, France.
- 15 Clinical Immunology Department, Saint Louis Hospital, AP-HP, Paris Cité University, Paris, France.
- 16 Imagine Institute, INSERM UMR1163, Paris Cité University, Paris, France; Pediatric Immunology-Hematology and Rheumatology Unit, Necker Hospital for Sick Children, AP-HP, Paris Cité University, Paris, France.
- 17 Department of Hematology, Amiens University Hospital, Amiens, France.
- 18 Department of Pediatrics, Kremlin-Bicêtre University Hospital, Kremlin-Bicêtre Centre University, AP-HP, Kremlin-Bicêtre, France.
- 19 Department of Dermatology, Strasbourg Centre University, Strasbourg, France.
- 20 Data Science Platform, Imagine Institute, INSERM UMR1163, Paris Cité University, Paris, France.
- 21 Imagine Institute, INSERM UMR1163, Paris Cité University, Paris, France; Department of Hematology, Necker Hospital for Sick Children, AP-HP, Paris Cité University, Paris, France.
- 22 Pediatric Immunology-Hematology and Rheumatology Unit, Necker Hospital for Sick Children, AP-HP, Paris Cité University, Paris, France.
- 23 Department of Dermatology, Reference Center for Genodermatoses (MAGEC), Necker Hospital for Sick Children, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris Cité University, Paris, France; Imagine Institute, INSERM UMR1163, Paris Cité University, Paris, France.
- 24 Laboratory of Human Genetics of Infectious Diseases, Necker Branch, INSERM, Necker Hospital for Sick Children, Paris Cité University, Paris, France; Imagine Institute, INSERM UMR1163, Paris Cité University, Paris, France; Pediatric Immunology-Hematology and Rheumatology Unit, Necker Hospital for Sick Children, AP-HP, Paris Cité University, Paris, France.
- 25 Department of Dermatology, Reference Center for Genodermatoses (MAGEC), Necker Hospital for Sick Children, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris Cité University, Paris, France; Imagine Institute, INSERM UMR1163, Paris Cité University, Paris, France. Electronic address: laura.polivka@aphp.fr.
- PMID: 39343308
- DOI: 10.1016/j.jaad.2024.09.029
Item in Clipboard
Dupilumab in atopic-dermatitis-like eczema associated with inborn errors of immunity: A nationwide study
Claire Guillemin et al.
J Am Acad Dermatol.
2025 Jan.
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Format
doi: 10.1016/j.jaad.2024.09.029.
Epub 2024 Sep 27.
Authors
Claire Guillemin
1
, Nathalia Bellon
1
, Marie Jachiet
2
, Sébastien Barbarot
3
, Emmanuelle Bourrat
4
, Christine Chiaverini
5
, Pierre Cougoul
6
, Mikaël Ebbo
7
, Mathilde Herber
8
, Thomas Hubiche
5
, Stéphanie Mallet
9
, Marie Tauber
10
, Vivien Béziat
11
, Martin Castelle
12
, Aurélie Du Thanh
13
, Johathan Farhi
14
, Claire Fieschi
15
, Benjamin Fournier
16
, Clément Gourguechon
17
, Tamazoust Guiddir
18
, Dan Lipsker
19
, Nadia Raison-Peyron
13
, Nicolas Garcelon
20
, Morgane Cheminant
21
, Felipe Suarez
21
, Olivier Hermine
21
, Stéphane Blanche
22
, Despina Moshous
16
, Nizar Mahlaoui
12
, Benedicte Neven
16
, Christine Bodemer
23
, Romain Lévy
24
, Laura Polivka
25
; Groupe de Recherche de la Société Française de Dermatologie Pédiatrique (GR SFDP); French Atopic Dermatitis Network from the Groupe de Recherche sur l’Eczéma Atopique (GREAT)
Affiliations
- 1 Department of Dermatology, Reference Center for Genodermatoses (MAGEC), Necker Hospital for Sick Children, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris Cité University, Paris, France.
- 2 Department of Dermatology, Saint-Louis Hospital, AP-HP, Paris Cité University, Paris, France.
- 3 Department of Dermatology, Nantes University, CHU Nantes, INRAE, UMR 1280, PhAN, Nantes, France.
- 4 Department of Dermatology, Reference Center for Genodermatoses (MAGEC), Saint Louis Hospital, AP-HP, Paris Cité University, Paris, France.
- 5 Department of Dermatology, Reference Center for Rare Dermatological Diseases (CRMRD), Nice Center University, Nice, France.
- 6 Department of Internal Medicine, Toulouse University Cancer Institute (IUCT) Oncopole, Toulouse, France.
- 7 Department of Internal Medicine, La Timone Hospital, Aix-Marseille University, Assistance Publique -Hôpitaux de Marseille (AP-HM), Marseille, France.
- 8 Department of Internal Medicine, Strasbourg Centre University, Strasbourg, France.
- 9 Department of Dermatology, La Timone Hospital, Aix-Marseille University, AP-HM, Marseille, France.
- 10 Department of Allergology and Clinical Immunology, HCL, Lyon Sud Center University, CIRI Inserm U1111, Lyon, France.
- 11 Laboratory of Human Genetics of Infectious Diseases, Necker Branch, INSERM, Necker Hospital for Sick Children, Paris Cité University, Paris, France; Imagine Institute, INSERM UMR1163, Paris Cité University, Paris, France.
- 12 French National Reference Center for Primary Immunodeficiencies (CEREDIH), Necker Hospital for Sick Children, AP-HP, Paris, France; Pediatric Immunology-Hematology and Rheumatology Unit, Necker Hospital for Sick Children, AP-HP, Paris Cité University, Paris, France.
- 13 Department of Dermatology, Montpellier Center University, Paris, France.
- 14 Department of Hematology, Angers Center University, Angers, France.
- 15 Clinical Immunology Department, Saint Louis Hospital, AP-HP, Paris Cité University, Paris, France.
- 16 Imagine Institute, INSERM UMR1163, Paris Cité University, Paris, France; Pediatric Immunology-Hematology and Rheumatology Unit, Necker Hospital for Sick Children, AP-HP, Paris Cité University, Paris, France.
- 17 Department of Hematology, Amiens University Hospital, Amiens, France.
- 18 Department of Pediatrics, Kremlin-Bicêtre University Hospital, Kremlin-Bicêtre Centre University, AP-HP, Kremlin-Bicêtre, France.
- 19 Department of Dermatology, Strasbourg Centre University, Strasbourg, France.
- 20 Data Science Platform, Imagine Institute, INSERM UMR1163, Paris Cité University, Paris, France.
- 21 Imagine Institute, INSERM UMR1163, Paris Cité University, Paris, France; Department of Hematology, Necker Hospital for Sick Children, AP-HP, Paris Cité University, Paris, France.
- 22 Pediatric Immunology-Hematology and Rheumatology Unit, Necker Hospital for Sick Children, AP-HP, Paris Cité University, Paris, France.
- 23 Department of Dermatology, Reference Center for Genodermatoses (MAGEC), Necker Hospital for Sick Children, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris Cité University, Paris, France; Imagine Institute, INSERM UMR1163, Paris Cité University, Paris, France.
- 24 Laboratory of Human Genetics of Infectious Diseases, Necker Branch, INSERM, Necker Hospital for Sick Children, Paris Cité University, Paris, France; Imagine Institute, INSERM UMR1163, Paris Cité University, Paris, France; Pediatric Immunology-Hematology and Rheumatology Unit, Necker Hospital for Sick Children, AP-HP, Paris Cité University, Paris, France.
- 25 Department of Dermatology, Reference Center for Genodermatoses (MAGEC), Necker Hospital for Sick Children, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris Cité University, Paris, France; Imagine Institute, INSERM UMR1163, Paris Cité University, Paris, France. Electronic address: laura.polivka@aphp.fr.
- PMID: 39343308
- DOI: 10.1016/j.jaad.2024.09.029
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No abstract available
Keywords: IEI; IL-4; atopic dermatitis; dupilumab; inborn errors of immunity; primary atopic disorders.
Conflict of interest statement
Conflicts of interest None disclosed.
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