Autoimmune Biliary Diseases: A Review of Primary Biliary Cholangitis, Primary Sclerosing Cholangitis, Immunoglobulin G4-Related Sclerosing Cholangitis, and Autoimmune Hepatitis
- PMID: 39448126
- DOI: 10.1016/j.suc.2024.04.010
Autoimmune Biliary Diseases: A Review of Primary Biliary Cholangitis, Primary Sclerosing Cholangitis, Immunoglobulin G4-Related Sclerosing Cholangitis, and Autoimmune Hepatitis
Abstract
Autoimmune and immune-mediated biliary diseases represent a small proportion of biliary disorders, but owing to their progressive nature, lead to end-stage liver disease, necessitating liver transplantation for definitive management.
Keywords: Autoimmune cholangiopathy; Autoimmune hepatitis; Biliary disease; Cholestasis; IgG4-related sclerosing cholangitis; Primary biliary cholangitis; Primary sclerosing cholangitis.
Copyright © 2024 Elsevier Inc. All rights reserved.
Conflict of interest statement
Disclosure The authors have nothing to disclose.
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