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Editorial
. 2024 Oct 1;13(5):875-878.
doi: 10.21037/hbsn-24-442. Epub 2024 Sep 26.

New guidelines for screening, evaluation and management of hepatobiliary disease in cystic fibrosis

P Aiden McCormick  1   2 , Emer Fitzpatrick  2   3
Affiliations
Editorial

New guidelines for screening, evaluation and management of hepatobiliary disease in cystic fibrosis

P Aiden McCormick et al. Hepatobiliary Surg Nutr. .
No abstract available

Keywords: Cirrhosis; hepatobiliary; non-cirrhotic portal hypertension; oesophageal varices; porto-sinusoidal vascular disease.

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Conflict of interest statement

Conflicts of Interest: Both authors have completed the ICMJE uniform disclosure form (available at https://hbsn.amegroups.com/article/view/10.21037/hbsn-24-442/coif). E.F. reports a grant to continue a longitudinal database of those with CF in Ireland to determine prevalence of liver disease and risk factors [payment made to institution (UCD) to employ research staff and contribute to the database]. The other author has no conflicts of interest to declare.

Figures

Figure 1
Figure 1
Pathophysiology of cystic fibrosis liver disease compared to other cirrhotic liver diseases. Portal hypertension occurs early due to obliterative portal venopathy and nodular regenerative hyperplasia. Cirrhosis develops late as a result of portal-based inflammation and fibrosis. CF, cystic fibrosis; AIH, autoimmune hepatitis; PBC, primary biliary cirrhosis; MASLD, metabolic associated steatotic liver disease.
See this image and copyright information in PMC

Comment on

References

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