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Case Reports
. 2024 Nov-Dec;29(6):630-633.
doi: 10.4103/jiaps.jiaps_108_24. Epub 2024 Nov 5.

Successful Surgical Repair of Complete Pentalogy of Cantrell

Madhumohan Reddy Basarahalli  1 , Daedeepya Alluri  2 , Srinivas Kini  3 , Ashish Sapre  4
Affiliations
Case Reports

Successful Surgical Repair of Complete Pentalogy of Cantrell

Madhumohan Reddy Basarahalli et al. J Indian Assoc Pediatr Surg. 2024 Nov-Dec.

Abstract

Pentalogy of Cantrell (PC) presents a distinctive challenge for clinicians and surgeons. In this case report, we have discussed the presentation, management, and literature review of a case of PC in a 17-month-old female child. The child was successfully managed with single-stage operation by a multidisciplinary team without any postoperative complications.

Keywords: Case report; multidisciplinary team; pentalogy of Cantrell.

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Conflict of interest statement

There are no conflicts of interest.

Figures

Figure 1
Figure 1
(a) The clincal photograph showing large omphalocele (green arrow) and (b) intra operative photograph showing pericardial defect (green arrow)
Figure 2
Figure 2
(a) Defect in sternum, (b) herniation of abdominal contents, (c) absent pericardium, and (d) defect at diaphragm
See this image and copyright information in PMC

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