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Case Reports
. 2024 Dec 25;17(4):437-439.
doi: 10.3400/avd.cr.24-00108. Epub 2024 Oct 29.

Pinhole Descending Aortic Rupture with Systemic Sclerosis and Dermatomyositis: A Case Report

Norihiro Ando  1 , Ryuichi Nabeshima  1 , Taiki Ito  1 , Koji Sato  1 , Hiroshi Sugiki  1
Affiliations
Case Reports

Pinhole Descending Aortic Rupture with Systemic Sclerosis and Dermatomyositis: A Case Report

Norihiro Ando et al. Ann Vasc Dis. .

Abstract

Thoracic descending aortic perforation with overlap syndrome (systemic sclerosis and dermatomyositis) is a rare, unreported vascular pathology. We describe the case of a 75-year-old woman who presented with chest tightness, back pain, and dyspnea. Computed tomography revealed a pinhole rupture in the descending aorta. The patient underwent a thoracic endovascular aortic repair and left chest drainage. Her postoperative course was uneventful.

Keywords: overlap syndrome; pinhole; thoracic aortic rupture.

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Figures

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Fig. 1 Preoperative enhanced CT showing thoracic descending pinhole aortic rupture (arrow). (A) Axial view. (B) Coronal view. (C) Three-dimensional-CT. AsAo: ascending aorta; CT: computed tomography; DAo: descending aorta
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Fig. 2 Three-dimensional CT of the aorta prior to patient discharge. AsAo: ascending aorta; DAo: descending aorta; CT: computed tomography
See this image and copyright information in PMC

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