Fatal splenic rupture in Ehlers-Danlos syndrome
- PMID: 3983062
- PMCID: PMC2418189
- DOI: 10.1136/pgmj.61.713.259
Fatal splenic rupture in Ehlers-Danlos syndrome
Abstract
A fatal case of Ehlers-Danlos syndrome (Type IV) is described. Autopsy revealed splenic rupture that had resulted from spontaneous haemorrhage into the splenic parenchyma. This is a previously unrecorded complication of Ehlers-Danlos syndrome and should be considered in the differential diagnosis of chest and abdominal pain in patients with this condition.
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