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. 2024;31(2):382-387.
doi: 10.15388/Amed.2024.31.2.14. Epub 2024 Dec 4.

Spontaneous Resolution of Congenital Intrahepatic Portosystemic Shunt

Taraprasad Tripathy  1 , Sandeep Behera  1 , Ranjan Patel  1 , Tanmay Dutta  2 , Aditi Kumar  3 , Amit Kumar Satpathy  3
Affiliations

Spontaneous Resolution of Congenital Intrahepatic Portosystemic Shunt

Taraprasad Tripathy et al. Acta Med Litu. 2024.

Abstract
in English, Italian

Congenital portosystemic shunts (CPSS) are a rare type of congenital abnormality. It results from abnormal embryonic development by the fourth week of fetal life. Congenital portosystemic shunts are believed to signify persistent communication between the portal and vitelline venous systems. Both extrahepatic and intrahepatic shunts are possible. They may develop on their own or in association with other congenital abnormalities. With regard to shunt type and size, symptoms vary widely. The anatomy of the shunt and associated abnormalities can be assessed by computed tomography and magnetic resonance angiography. The treatment plan is based on the type of shunt, its location and level of function, the patient's age, and the severity of their symptoms.

įgimtas portosisteminis šuntas (angl. Congenital portosystemic shunts, CPSS) yra reta įgimta anomalija. Ji atsiranda dėl netaisyklingo embriono vystymosi iki ketvirtos vaisiaus gyvenimo savaitės. Manoma, kad įgimti portosisteminiai šuntai reiškia nuolatinį portalinės ir stiklakūnio venų sistemos ryšį. Galimi tiek ekstrahepatiniai, tiek intrahepatiniai šuntai. Jie gali išsivystyti atskirai arba kartu su kitomis įgimtomis anomalijomis. Atsižvelgiant į šunto tipą ir dydį, simptomai labai skiriasi. Šunto anatomiją ir susijusias anomalijas galima įvertinti kompiuterinės tomografijos ir magnetinio rezonanso angiografijos metodais. Gydymo planas sudaromas atsižvelgiant į šunto tipą, jo vietą ir funkcijos lygį, paciento amžių ir simptomų sunkumą.

Keywords: Abernathy malformation; congenital portosystemic shunts; embolization.

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Conflict of interest statement

None to declare

Figures

Figure 1
Figure 1
a) USG shows anechoic tubular structure communicating between left portal vein and right hepatic vein. b) On color Doppler there is communication between hepatic vein and portal vein which shows color flow with aliasing. c) Calculation of porto-venous shunt ratio is shown – ~88% in present case.
Figure 2
Figure 2
a) and b). CECT porto-venous phase MIP images show communication between branch portal vein and right hepatic vein – suggestive of type 2 congenital portosystemic shunt. b) Follow-up USG after 2 months of presentation shows resolution of shunt. Porto-venous shunt ratio is ~20.1%. (MIP: Maximum intensity projection)
See this image and copyright information in PMC

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