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Case Reports
. 2024 Dec;16(Suppl 5):S4914-S4916.
doi: 10.4103/jpbs.jpbs_1249_24. Epub 2025 Jan 30.

A Rare Clinical Presentation of Pediatric Hypertension due to Unilateral Renal Artery Stenosis with the Middle Aortic Syndrome

Affiliations
Case Reports

A Rare Clinical Presentation of Pediatric Hypertension due to Unilateral Renal Artery Stenosis with the Middle Aortic Syndrome

Bala Vigneshwaran et al. J Pharm Bioallied Sci. 2024 Dec.

Abstract

Renal artery stenosis is one of the secondary causes of pediatric hypertension. Cases with critical unilateral renal artery stenosis associated with the middle aortic syndrome are rare phenomena. The middle aortic syndrome (MAS) is a rare vascular disease representing an important cause of severe hypertension in children. MAS are mostly idiopathic, but also may occur in genetic and acquired disorders.

Keywords: Middle aortic syndrome; pediatric hypertension; renal artery stenosis; renovascular disease.

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Conflict of interest statement

There are no conflicts of interest.

Figures

Figure 1
Figure 1
CECT Renal Angiogram
Figure 2
Figure 2
Renal Perfusion Angiography showing Left Renal artery Stenosis
Figure 3
Figure 3
CECT angiogram showing Left Renal artery stenosis
Figure 4
Figure 4
CECT Renal angiogram Showing introduction Balloon for Renal artery Dilation
Figure 5
Figure 5
CECT Renal angiogram Showing stenotic dilatation post Balloon angioplasty for stenotic Left Renal artery

References

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