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Case Reports
. 2025 Feb 7:58:74-76.
doi: 10.1016/j.jdcr.2024.12.040. eCollection 2025 Apr.

Atypical bullous systemic lupus erythematosus with features of linear IgA bullous dermatosis

Roy Jiang  1 , Amanda G Zhou  1 , Christine J Ko  1 , Michael Girardi  1 , Ailish Hanly  1 , Catherine Xie  1 , Ana Preda-Naumescu  1 , Jeffrey R Gehlhausen  1 , Mary M Tomayko  1   2
Affiliations
Case Reports

Atypical bullous systemic lupus erythematosus with features of linear IgA bullous dermatosis

Roy Jiang et al. JAAD Case Rep. .
No abstract available

Keywords: bullous SLE; immunobullous disorder; linear IgA dermatosis.

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Conflict of interest statement

None disclosed.

Figures

Fig 1
Fig 1
Initial presentation. (A) Exam findings on initial presentation of scattered vesicles and bullae on pink pruritic plaques over the back. (B) Initial H&E of skin biopsy sample showing subepidermal acantholysis and neutrophilic infiltrate at the DEJ. DEJ, Dermal-epidermal junction.
Fig 2
Fig 2
IgA immunofluorescence studies. (A) DIF showing linear IgA deposition along DEJ. (B) Dermal side IgA staining on DIF performed on SSS processed initial skin biopsy sample. DEJ, Dermal-epidermal junction; DIF, direct immunofluorescence; SSS, salt split skin.
See this image and copyright information in PMC

References

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