[Pseudo precocious puberty in the McCune-Albright syndrome]
- PMID: 4022718
[Pseudo precocious puberty in the McCune-Albright syndrome]
Abstract
McCune Albright Syndrome is characterized by the triad of polyostostic fibrous dysplasia of bones, skin pigmentation (café au lait-spots) and sexual precocity. The authors report a case of a 7 years girl with this syndrome in whom the sexual precocity is due to an autonomous hyperfunctioning of luteinized follicular cysts of ovary. The pathogenic mechanisms of this autonomy are debate.
Similar articles
-
McCune Albright Syndrome (MCAS): a case series.Indian Pediatr. 2003 Jan;40(1):29-35. Indian Pediatr. 2003. PMID: 12554915
-
Treatment of precocious puberty in the McCune-Albright syndrome with the aromatase inhibitor testolactone.N Engl J Med. 1986 Oct 30;315(18):1115-9. doi: 10.1056/NEJM198610303151802. N Engl J Med. 1986. PMID: 3093862
-
[Precocious puberty caused by McCune-Albright syndrome in a girl aged 6 years and 9 months].Endokrynol Diabetol Chor Przemiany Materii Wieku Rozw. 2006;12(1):63-7. Endokrynol Diabetol Chor Przemiany Materii Wieku Rozw. 2006. PMID: 16704864 Polish.
-
McCune-Albright syndrome in adulthood.Pediatr Endocrinol Rev. 2007 Aug;4 Suppl 4:453-62. Pediatr Endocrinol Rev. 2007. PMID: 17982395 Review.
-
Fibrous dysplasia with intramuscular myxoma (Mazabraud's syndrome). Report of a case and review of the literature.Rev Rhum Engl Ed. 1999 Mar;66(3):180-3. Rev Rhum Engl Ed. 1999. PMID: 10327500 Review.
Publication types
MeSH terms
LinkOut - more resources
Medical