Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
Case Reports
. 2025 May 22;20(1):235.
doi: 10.1186/s13019-025-03344-7.

Cone reconstruction after carpentier repair in ebstein anomaly: yes we can!

Alessandro Giamberti  1 , Federica Torchio  2 , Massimo Chessa  3   4 , Stefan Veljkovic  5 , Ana Perunicic  5 , Aleksandra Nikolic  5
Affiliations
Case Reports

Cone reconstruction after carpentier repair in ebstein anomaly: yes we can!

Alessandro Giamberti et al. J Cardiothorac Surg. .

Abstract

The management of recurrent tricuspid regurgitation (TR) after initial tricuspid valve (TV) repair in patients with Ebstein's anomaly (EA) represents a complex challenge. Traditionally, tricuspid valve replacement has been the first-line option for these patients. The use of Cone Repair for recurrent TR remains under-reported. Herein, we report a successful cone repair for recurrent TR, twelve years after a Carpentier repair in a 39-year-old male patient.

Keywords: Adult with congenital heart disease; Cardiac surgery; Cone repair; Ebstein’s anomaly.

PubMed Disclaimer

Conflict of interest statement

Declarations. Conflict of interest: The authors declare that they have no known competing financial interests or personal relationships that could have appeared to influence the work reported in this paper. Ethics approval and consent to participate: Not applicable. Competing interests: The authors declare no competing interests. Consent for publication: Written informed consent was obtained from the patient for publication of this case report and accompanying images. All the authors agree to the publication of the article.

Figures

Fig. 1
Fig. 1
Pre-operative apical 4-chamber echocardiography showing typical features of EA with apical displacement (46 mm) of the septal leaflet. RA, right atrium; aRV, atrialised right ventricle; fRV, functional right ventricle; LA, left atrium; LV, left ventricle; * septal leaflet
Fig. 2
Fig. 2
Magnetic resonance cine-SSFP images in long axis. Special focus on the tricuspid valve and apical displacement of the septal leaflet. RA, right atrium; aRV, atrialised right ventricle; fRV, functional right ventricle; LA, left atrium; LV, left ventricle; * septal leaflet
Fig. 3
Fig. 3
Intra-operative view showing the reattachment of the cone and the leaflet augmentation with heterologous pericardial patch
See this image and copyright information in PMC

References

    1. Attenhofer Jost CH, Connolly HM, Dearani JA, Edwards WD, Danielson GK. Ebstein’s anomaly. Circulation. 2007;115(2):277–85. - PubMed
    1. Pasqualin G, Boccellino A, Chessa M, Ciconte G, Marcolin C, Micaglio E, Pappone C, Sturla F, Giamberti A. Ebstein’s anomaly in children and adults: multidisciplinary insights into imaging and therapy. Heart. 2024;110:235–44. - PMC - PubMed
    1. Hunter SW, Lillehei CW. Ebstein’s malformation of the tricuspid valve; study of a case together with suggestion of a new form of surgical therapy. Dis Chest. 1958;33:297–304. - PubMed
    1. Danielson GK, Fuster V. Surgical repair of Ebstein’s anomaly. Ann Surg. 1982;196:499–504. - PMC - PubMed
    1. Carpentier A, Chauvaud S, Mace L, Relland J, Mihaileanu S, Marino JP, Abry B, Guibourt P. A new reconstructive operation for Ebstein’s anomaly of the tricuspid valve. J Thorac Cardiovasc Surg. 1988;96:92–101. - PubMed

Publication types

LinkOut - more resources