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. 2025 Apr 3;30(4):203-211.
doi: 10.1093/pch/pxae102. eCollection 2025 Jul.

Primary ciliary dyskinesia

Vincent Lavoie  1 , Zofia Zysman-Colman  1 , Adam J Shapiro  1   2
Affiliations

Primary ciliary dyskinesia

Vincent Lavoie et al. Paediatr Child Health. .
No abstract available

Keywords: Bronchiectasis; Primary ciliary dyskinesia; Situs inversus totalis.

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Figures

Figure 1.
Figure 1.
Ultrastructure of a normal ciliary axoneme. Cross-section of a normal ciliary axoneme with 9 + 2 configurations, showing the various ultrastructural components that power ciliary beat (outer and inner dynein arms), drive normal axonemal formation along its length (nexin-dynein regulatory links), and provide best stability (radial spokes and central apparatus).
Figure 2.
Figure 2.
American Thoracic Society suggested algorithm for evaluating patients with suspected primary ciliary dyskinesia. Reprinted with permission of the American Thoracic Society. Copyright © 2024 American Thoracic Society. All rights reserved (36,37). The American Journal of Respiratory and Critical Care Medicine is an official journal of the American Thoracic Society.
See this image and copyright information in PMC

References

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