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Case Reports
. 1979 Apr;100(4):409-16.
doi: 10.1111/j.1365-2133.1979.tb01641.x.

Keratosis pilaris atrophicans faciei (ulerythema ophryogenes): a cutaneous marker in the Noonan syndrome

D O Pierini, A M Pierini
Case Reports

Keratosis pilaris atrophicans faciei (ulerythema ophryogenes): a cutaneous marker in the Noonan syndrome

D O Pierini et al. Br J Dermatol. 1979 Apr.

Abstract

Five cases are reported of Noonan's syndrome, all of which presented keratosis pilaris atrophicans faciei (ulerythema ophryogenes). This dermatosis fulfils the criteria mentioned by Noonan & Ehmke (1963) as a pointer for the investigation of cardiac anomalies, especially of the pulmonary artery.

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